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Issue DateTitleAuthor(s)TypeAccess
12019Restoring brain cholesterol turnover improves autophagy and has therapeutic potential in mouse models of spinocerebellar ataxiaNóbrega, Clévio David Rodrigues ; Mendonça, Liliana Simões ; Marcelo, Adriana Isabel do Vale ; Lamazière, Antonin; Tomé, Sandra Marisa Oliveira ; Despres, Gaetan; Matos, Carlos A; Mechmet, Fatich; Langui, Dominique; den Dunnen, Wilfred; Almeida, Luís Pereira de ; Cartier, Nathalie; Alves, Sandro José Paiva Fernandes articleembargoedAccess
221-Aug-2014RNA Interference Mitigates Motor and Neuropathological Deficits in a Cerebellar Mouse Model of Machado-Joseph DiseaseNóbrega, Clévio ; Nascimento-Ferreira, Isabel ; Onofre, Isabel ; Albuquerque, David ; Déglon, Nicole ; Almeida, Luís Pereira de articleopenAccess
325-Aug-2021The autophagy-enhancing drug carbamazepine improves neuropathology and motor impairment in mouse models of Machado-Joseph diseaseVasconcelos-Ferreira, Ana ; Carmo-Silva, Sara; Codêsso, José Miguel Antunes ; Silva, Patrick Joel da ; Martinez, Alberto Rolim Muro; França, Marcondes Cavalcante; Nóbrega, Clévio David Rodrigues ; Almeida, Luís Pereira de articleembargoedAccess
429-Nov-2021Autophagy in Spinocerebellar ataxia type 2, a dysregulated pathway, and a target for therapyMarcelo, Adriana ; Afonso, Inês T.; Afonso-Reis, Ricardo; Brito, David V. C.; Costa, Rafael G.; Rosa, Ana; Alves-Cruzeiro, João ; Ferreira, Benedita; Henriques, Carina; Nobre, Rui J. ; Matos, Carlos A.; Almeida, Luís Pereira de ; Nóbrega, Clévio articleopenAccess
58-Jun-2021Stress granules, RNA-binding proteins and polyglutamine diseases: too much aggregation?Marcelo, Adriana ; Koppenol, Rebekah; Almeida, Luís Pereira de ; Matos, Carlos A.; Nóbrega, Clévio articleopenAccess
69-Apr-2020Trehalose alleviates the phenotype of Machado-Joseph disease mouse modelsSantana, Magda M. ; Paixão, Susana ; Cunha-Santos, Janete; Silva, Teresa Pereira ; Trevino-Garcia, Allyson; Gaspar, Laetitia da Silva ; Nóbrega, Clévio ; Nobre, Rui J. ; Cavadas, Cláudia ; Greif, Hagar; Almeida, Luís Pereira de articleopenAccess
72013Silencing mutant ataxin-3 rescues motor deficits and neuropathology in Machado-Joseph disease transgenic miceNóbrega, Clévio ; Nascimento-Ferreira, Isabel ; Onofre, Isabel ; Albuquerque, David ; Hirai, Hirokazu; Déglon, Nicole ; Almeida, Luís Pereira de articleopenAccess
82011Moderate long-term modulation of neuropeptide Y in hypothalamic arcuate nucleus induces energy balance alterations in adult ratsSousa-Ferreira, Lígia ; Garrido, Manuel Joaquim Marques ; Nascimento-Ferreira, Isabel ; Nóbrega, Clévio ; Carvalho, Ana dos Santos ; Álvaro, Ana Rita Costa Silva ; Salgado, Joana Rosmaninho ; Kaster, Manuella; Kügler, Sebastian ; Almeida, Luís Pereira de ; Cavadas, Cláudia articleopenAccess
91-Jun-2023The stress granule protein G3BP1 alleviates spinocerebellar ataxia-associated deficitsKoppenol, Rebekah; Conceição, André ; Afonso, Inês T.; Afonso-Reis, Ricardo; Costa, Rafael G.; Tomé, Sandra ; Teixeira, Diogo ; da Silva, Joana Pinto; Codêsso, José Miguel ; Brito, David V. C.; Mendonça, Liliana ; Marcelo, Adriana ; Almeida, Luís Pereira de ; Matos, Carlos A.; Nóbrega, Clévio articleopenAccess