Please use this identifier to cite or link to this item:
https://hdl.handle.net/10316/108946
DC Field | Value | Language |
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dc.contributor.author | Alves, Ana | - |
dc.contributor.author | Alfaro, Tiago M. | - |
dc.contributor.author | Madama, Daniela | - |
dc.contributor.author | Freitas, Sara | - |
dc.contributor.author | Cordeiro, Carlos Robalo | - |
dc.contributor.author | Gamboa, Fernanda | - |
dc.date.accessioned | 2023-09-26T09:06:45Z | - |
dc.date.available | 2023-09-26T09:06:45Z | - |
dc.date.issued | 2015 | - |
dc.identifier.issn | 1646-0758 | pt |
dc.identifier.issn | 0870-399X | pt |
dc.identifier.uri | https://hdl.handle.net/10316/108946 | - |
dc.description.abstract | A amiloidose caracteriza-se pela deposição extracelular de substância amilóide em diferentes órgãos e tecidos. O atingimento pulmonar é raro e pode acontecer de forma isolada ou associado a doença sistémica. Descrevem-se dois casos clínicos. Caso 1: Mulher de 71 anos, com antecedentes de bronquiectasias e síndrome de Sjögren, que referia anorexia, emagrecimento e tosse produtiva. O estudo incluiu uma biópsia pulmonar cirúrgica que demonstrou amiloidose localizada ao aparelho respiratório. Caso 2: Homem de 83 anos, ex-fumador, assintomático. Enviado por opacidade nodular em radiografia de tórax de rotina. A biópsia pulmonar transtorácica revelou um tumor amilóide do pulmão (amiloidoma). Estes casos ilustram uma doença rara que no Caso 1 está associada a bronquiectasias e síndrome de Sjögren. O diagnóstico diferencial mais importante é a patologia neoplásica, sendo o diagnóstico definitivo importante, já que a amiloidose pulmonar é geralmente benigna e indolente. | pt |
dc.description.abstract | Amyloidosis is characterized by amyloid extracellular deposition in organs and tissues. Pulmonary involvement is a rare manifestation of the disease and it can be focal or as part of systemic amyloidosis. We report two cases. Case 1: 71 year-old female with bronchiectasis and Sjogren’s syndrome, who complained of anorexia, weight loss and a productive cough. The diagnostic study included a surgical lung biopsy and histological examination demonstrated pulmonary amyloidosis. Case 2: 83 year-old male patient, ex-smoker, asymptomatic, whose routine chest x-ray showed a nodular opacity in the right lung field. A transthoracic biopsy revealed an amyloid lung tumor. These cases illustrate a rare disease which in Case 1 also coexisted with Sjögren’s syndrome and bronchiectasis. The most important differential diagnosis is cancer and so a definitive diagnosis is essential, as amyloidosis is usually benign and indolent. | pt |
dc.language.iso | por | pt |
dc.publisher | Ordem dos Medicos | pt |
dc.rights | openAccess | pt |
dc.rights.uri | http://creativecommons.org/licenses/by-nc/4.0/ | pt |
dc.subject | Amiloidose | pt |
dc.subject | Bronquiectasias; | pt |
dc.subject | Doenças do Pulmão | pt |
dc.subject | Síndrome de Sjögren | pt |
dc.subject | Amyloidosis | pt |
dc.subject | Bronchiectasis | pt |
dc.subject | Lung Diseases | pt |
dc.subject | Sjögren’s Syndrome | pt |
dc.title | Amiloidose Pulmonar: Um Desafio Diagnóstico | pt |
dc.title.alternative | Pulmonary Amyloidosis: A Diagnostic Challenge | pt |
dc.type | article | - |
degois.publication.firstPage | 530 | pt |
degois.publication.lastPage | 533 | pt |
degois.publication.issue | 4 | pt |
degois.publication.title | Acta Medica Portuguesa | pt |
dc.peerreviewed | yes | pt |
dc.identifier.doi | 10.20344/amp.5948 | pt |
degois.publication.volume | 28 | pt |
dc.date.embargo | 2015-01-01 | * |
uc.date.periodoEmbargo | 0 | pt |
item.fulltext | Com Texto completo | - |
item.grantfulltext | open | - |
item.languageiso639-1 | pt | - |
item.cerifentitytype | Publications | - |
item.openairetype | article | - |
item.openairecristype | http://purl.org/coar/resource_type/c_18cf | - |
crisitem.author.researchunit | iNOVA4Health - Programme in Translational Medicine (iBET, CEDOC/FCM, IPOLFG and ITQB) | - |
crisitem.author.orcid | 0000-0002-8264-3856 | - |
Appears in Collections: | FMUC Medicina - Artigos em Revistas Nacionais |
Files in This Item:
File | Description | Size | Format | |
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Pulmonary-amyloidosis-A-diagnostic-challengeActa-Medica-Portuguesa.pdf | 2.31 MB | Adobe PDF | View/Open |
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This item is licensed under a Creative Commons License